ABSTRACT

Rhombencephalosynapsis is a malformation characterized the fusion of cerebral vermis agenesis/hypogenesis and cerebral hemisphere. Less than 50 cases are reported until now, and adult cases are even more rare. In these patients different syptomps varying from truncal ataxia, mental reterdation to severe cerebral palsy can be observed though neurologic survey may result normal.There may not be a correlation between radiologic images and clinic. There was no abnormality in the neurologic examination of the 27 year old patient who consulted with headache complaints. It is determined in the cranial magnetic resonance imaging (MRG) images that there was no vermis and the cerebellar hemispheres are fusioned in the midline. We aimed to present Rhombensefalosinapsis because it is seen very rarely.