Basal Ganglia Affecting Due To Hepatocerebral Degeneration: Two Case Report
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Case Report
P: 51-52
September 2006

Basal Ganglia Affecting Due To Hepatocerebral Degeneration: Two Case Report

İstanbul Med J 2006;7(3):51-52
1. İstanbul Eğitim Ve Araştırma Hastanesi Nöroloji Kliniği
2. SB İstanbul Eğitim ve Araştırma Hastanesi, Nöroloji Kliniği, Asistanı
3. SB İstanbul Eğitim Ve Araştırma Hastanesi Nöroloji Kliniği
4. SSK İstanbul Hastanesi Nöroloji Kliniği
5. İstanbul Eğitim ve Araştırma Hastanesi, Nöroloji Kliniği,Uzmanı
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ABSTRACT

Chronic hepatocerebral degeneration is a disease affecting neurologic,hepatic or both of these systems.Clinical presentation includes neuropsychiatric symptoms, like ata.xia, chorea, bradykinesıa myoclonus, dystonia andı t can also includes a combination ofthese proofs. Improvements in neuroradiology showed that patients with liver impairment have hyperintens signals an putamen,pallidum and rarely an mesencephalon on MR, Tl Weight slides.Astrocitic dif.ferantation and manganese staragement are accused in ethiology.

We introduce two case with hepatocerbral de generatian presenting itself with ınvoluntary movements like chorea and cloudy conscious.

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