Laugier-Hunziker syndrome (LHS) is a rare, idiopathic, and benign cause of mucocutaneous pigmentation. Frequently, the oral mucosa, lips, and nails are involved. It is not associated with any underlying disease and is not premalignant. Diagnosis is confirmed by the exclusion of diseases that make mucocutaneous pigmentation. Herein, we have reported a 53-yearoldwoman diagnosed as having LHS, with longitudinal melanonychia and hyperpigmented macular lesions of the buccal mucosa. We reported this case, because this syndrome is rarely seen, and the differential diagnosis from other causes of mucocutaneous pigmentation is important.
Keywords: Laugier-Hunziker syndrome, melanonychia, mucocutaneous pigmentation