Original Investigation

Congenital Malformations of the Inner Ear: Evaluation with MRI and CT of the Temporal Bone

10.5152/imj.2014.09326

  • Göksel Tuzcu
  • Önder Turna
  • A. Hande Yardımcı
  • Engin Acıoğlu

İstanbul Med J 2014;15(3):171-174

Objective:

We aimed to present computed tomography (CT) and magnetic resonance imaging (MRI) findings of internal ear abnormalities detected at our clinics and to demonstrate the efficiency of MRI in determining abnormalities and nerve morbidities at these cases.

Methods:

Between July 2009-April 2011, 15 patients (9 females, 6 males) with a mean age of 5.7 (1-12) and a diagnosis of sensorineural hearing loss, assessed by temporal bone MDCT and MRI, were included in the study. The patients were retrospectively evaluated by using a picture archiving and communication system (PACS).

Results:

Mondini deformity was found in 7 (46%) of patients, and isolated large vestibular aquaduct was found in 5 (33%) patients. Michel deformity, cochlear aplasia, and common cavite anomaly were detected in 1 (7%), 1 (7%), and 1 (7%) patient, respectively.

Conclusion:

Structural inner ear anomalies are causes of congenital or progressive sensorineural hearing loss. MDCT and MRI have high diagnostic yield in detecting the anomalies of the inner ear in patients with congenital sensorineural hearing loss and have a valuable role in the management of these patients.

Keywords: Congenital, inner ear, Mondini, MRI